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词条 IgA pemphigus
释义

  1. History

  2. See also

  3. References

  4. External links

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}}{{see also|List of target antigens in pemphigus}}

IgA pemphigus is a subtype of pemphigus with two distinct forms:

  • Subcorneal pustular dermatosis (also known as Sneddon–Wilkinson disease and pustulosis subcornealis)[1] is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils.[2][3]{{rp|203}} This is distinct from and not to be confused with subcorneal pustular dermatosis type of IgA pemphigus. Sneddon's syndrome, also known as Ehrmann-Sneddon syndrome, is also a different syndrome.[4]
  • Intraepidermal neutrophilic IgA dermatosis is characterized histologically by intraepidermal bullae with neutrophils, some eosinophils, and acantholysis.[3]{{rp|465}}

History

Early descriptions were made by Darrell Wilkinson, a British dermatologist.[5]

See also

  • Pemphigus
  • List of cutaneous conditions
  • List of conditions caused by problems with junctional proteins
  • List of immunofluorescence findings for autoimmune bullous conditions

References

1. ^{{cite web|last1=RESERVED|first1=INSERM US14 -- ALL RIGHTS|title=Orphanet: Subcorneal pustular dermatosis|url=http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=48377|website=www.orpha.net|accessdate=8 March 2017|language=en}}
2. ^{{cite book|title=Fitzpatrick's dermatology in general medicine.|date=2003|publisher=McGraw-Hill|location=New York, NY [u.a.]|isbn=0-07-138076-0|pages=625|edition=6th|editor=Irwin M. Freedberg|display-editors=etal}}
3. ^James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. {{ISBN|0-7216-2921-0}}.
4. ^{{cite web|last1=Berlit|first1=Peter|title=Sneddon's Syndrome|url=http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=GB&Expert=820|website=Orphanet}}
5. ^{{Cite web|url=http://munksroll.rcplondon.ac.uk/Biography/Details/6188|title=Munks Roll Details for Peter Edward Darrell Sheldon Wilkinson|website=munksroll.rcplondon.ac.uk|access-date=2017-11-10}}

External links

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| eMedicineTopic = 1063776
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}}{{Genodermatoses-stub}}{{Vesiculobullous disease}}

1 : Chronic blistering cutaneous conditions

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