请输入您要查询的百科知识：

　

词条 Rapunzel syndrome
释义

  1. Signs and symptoms

  2. Diagnosis

  3. Treatment

  4. References

  5. Further reading

Rapunzel syndrome is an extremely rare intestinal condition in humans resulting from ingesting hair (trichophagia).[1][2] The syndrome is named after the long-haired girl Rapunzel in the fairy tale by the Brothers Grimm. Trichophagia is sometimes associated with the hair-pulling disorder trichotillomania.[3] This syndrome is a rare and unusual form of trichobezoar.[4]

Signs and symptoms

The use of the Rapunzel syndrome first appeared in the literature in 1968.[5]

Characteristics of the syndrome include:

  • The body of a trichobezoar (hairball) located in the stomach, and its tail (hence the reference to Rapunzel in the syndrome's name) in the small bowel and/or in the right colon
  • Small or large bowel obstruction
  • Occurring in psychiatric patients
  • Trichotillomania

Rapunzel Syndrome is caused by indigestion of hair.

Diagnosis

Trichobezoar can be preoperatively diagnosed. However, the diagnosis of the Rapunzel syndrome has to consider several aspects such as the patient's history with disorders like Trichophagia and Trichotillomania.[6][7]

The diagnosis of the syndrome is also done by endoscopy. A CT scan is recommended to determine the size and the extension of the trichobezoar.[5]

Treatment

Because the human gastrointestinal tract is unable to digest human hair, the trichobezoar may have to be treated surgically.

Patients usually also require psychiatric evaluation and treatment due to the association with impulse control disorders, especially trichotillomania.[8]

References

1. ^{{cite journal |vauthors=Sah DE, Koo J, Price VH |title=Trichotillomania |journal=Dermatol Ther |volume=21 |issue=1 |pages=13–21 |year=2008 |pmid=18318881 |doi=10.1111/j.1529-8019.2008.00165.x |url=http://www3.interscience.wiley.com/cgi-bin/fulltext/119418689/PDFSTART|format=PDF}}{{dead link|date=February 2019|bot=medic}}{{cbignore|bot=medic}}
2. ^{{cite journal |vauthors=Ventura DE, Herbella FA, Schettini ST, Delmonte C |title=Rapunzel syndrome with a fatal outcome in a neglected child |journal=J. Pediatr. Surg. |volume=40 |issue=10 |pages=1665–7 |year=2005 |pmid=16227005 |doi=10.1016/j.jpedsurg.2005.06.038}}
3. ^{{cite journal |vauthors=Chamberlain SR, Menzies L, Sahakian BJ, Fineberg NA |title=Lifting the veil on trichotillomania |journal=Am J Psychiatry |volume=164 |issue=4 |pages=568–74 |date=April 2007 |pmid=17403968 |doi=10.1176/appi.ajp.164.4.568 }}
4. ^{{Cite journal|last=Gonuguntla|first=Veena|last2=Joshi|first2=Divya-Devi|date=2009|title=Rapunzel Syndrome: A Comprehensive Review of an Unusual Case of Trichobezoar|journal=Clinical Medicine & Research|volume=7|issue=3|pages=99–102|doi=10.3121/cmr.2009.822|issn=1539-4182|pmc=2757434|pmid=19625498|via=}}
5. ^1 {{Cite book|url=https://books.google.com/?id=oVMTDgAAQBAJ&pg=PA150&dq=Rapunzel+syndrome#v=onepage&q=Rapunzel%20syndrome&f=false|title=The Medical Lives of History's Famous People|last=Maloney|first=William James|date=2014-09-22|publisher=Bentham Science Publishers|isbn=9781608059362|location=|pages=|language=en}}
6. ^{{Cite journal|last=Wang|first=Zhe|last2=Cao|first2=Feng|last3=Liu|first3=Diangang|last4=Fang|first4=Yu|last5=Li|first5=Fei|date=2016-11-22|title=The diagnosis and treatment of Rapunzel syndrome|journal=Acta Radiologica Open|volume=5|issue=11|pages=205846011562766|doi=10.1177/2058460115627660|issn=2058-4601|pmc=5122172|pmid=27900201}}
7. ^{{Cite journal|last=Wang|first=Zhe|last2=Cao|first2=Feng|last3=Liu|first3=Diangang|last4=Fang|first4=Yu|last5=Li|first5=Fei|date=2016-11-22|title=The diagnosis and treatment of Rapunzel syndrome|url=https://www.researchgate.net/publication/310734224|journal=Acta Radiologica Open|volume=5|issue=11|pages=205846011562766|doi=10.1177/2058460115627660|pmid=27900201|pmc=5122172}}
8. ^{{cite journal |vauthors=Gorter RR, Kneepkens CM, Mattens EC, Aronson DC, Heij HA |title=Management of trichobezoar: case report and literature review |journal=Pediatr. Surg. Int. |volume=26 |issue=5 |pages=457–63 |date=May 2010 |pmid=20213124 |pmc=2856853 |doi=10.1007/s00383-010-2570-0 |url=}}

Further reading

  • {{cite journal |vauthors=Duncan ND, Aitken R, Venugopal S, West W, Carpenter R |title=The Rapunzel syndrome. Report of a case and review of the literature |journal=West Indian Med J |volume=43 |issue=2 |pages=63–5 |date=June 1994 |pmid=7941500 }}
  • {{cite journal |vauthors=Levy RM, Komanduri S |title=Images in clinical medicine. Trichobezoar |journal=N. Engl. J. Med. |volume=357 |issue=21 |pages=e23 |date=November 2007 |pmid=18032760 |doi=10.1056/NEJMicm067796 |laysummary=http://www.cnn.com/2007/HEALTH/11/21/hairball.case/index.html|laysource=CNN|laydate=2007-11-22}}
  • {{cite journal |vauthors=Matejů E, Duchanová S, Kovac P, Moravanský N, Spitz DJ |title=Fatal case of Rapunzel syndrome in neglected child |journal=Forensic Sci. Int. |volume=190 |issue=1–3 |pages=e5–7 |date=September 2009 |pmid=19505779 |doi=10.1016/j.forsciint.2009.05.008}}
  • {{cite journal |vauthors=Pul N, Pul M |title=The Rapunzel syndrome (trichobezoar) causing gastric perforation in a child: a case report |journal=Eur. J. Pediatr. |volume=155 |issue=1 |pages=18–9 |year=1996 |pmid=8750804 |doi=10.1007/bf02115620}}
{{disease-stub}}

2 : Diseases of intestines|Syndromes
随便看

　

开放百科全书收录14589846条英语、德语、日语等多语种百科知识，基本涵盖了大多数领域的百科知识，是一部内容自由、开放的电子版国际百科全书。

　

Copyright © 2023 OENC.NET All Rights Reserved
京ICP备2021023879号 更新时间：2024/9/20 8:56:24